Cystic Fibrosis

Disease references

Disease Ontology : DOID:1485

References (14)

Intestinal mucins from cystic fibrosis mice show increased fucosylation due to an induced Fucalpha1-2 glycosyltransferase. (2002)
Thomsson KA, Hinojosa-Kurtzberg M, Axelsson KA, Domino SE, Lowe JB, Gendler SJ, Hansson GC
Pubmed : 12164788   DOI : 10.1042/BJ20020371
Status : Reviewed

Sialylation and sulfation of the carbohydrate chains in respiratory mucins from a patient with cystic fibrosis. (1994)
Lo-Guidice J, Wieruszeski J, Lemoine J, Verbert A, Roussel P, Lamblin G
Pubmed : 8034632  
Status : Reviewed

Structures of sulfated oligosaccharides in human trachea mucin glycoproteins. (1993)
Sangadala S, Bhat U, Mendicino J
Pubmed : 8107688  
Status : Reviewed

Quantitation and structures of oligosaccharide chains in human trachea mucin glycoproteins. (1992)
Sangadala S, Bhat U, Mendicino J
Pubmed : 1488058  
Status : Reviewed

Sulfated sialyl-oligosaccharides derived from tracheobronchial mucous glycoproteins of a patient suffering from cystic fibrosis. (1992)
Mawhinney T, Landrum D, Gayer D, Barbero G
Pubmed : 1473102  
Status : Reviewed

Structure of two sulphated oligosaccharides from respiratory mucins of a patient suffering from cystic fibrosis. A fast-atom-bombardment m.s. and 1H-n.m.r. spectroscopic study. (1991)
Lamblin G, Rahmoune H, Wieruszeski J, Lhermitte M, Strecker G, Roussel P
Pubmed : 2018475  
Status : Reviewed

Additional fucosyl residues on membrane glycoproteins but not a secreted glycoprotein from cystic fibrosis fibroblasts. (1990)
Wang YM, Hare TR, Won B, Stowell CP, Scanlin TF, Glick MC, Hård K, van Kuik JA, Vliegenthart JF
Pubmed : 2387072  
Status : Reviewed

Structure of sialyl-oligosaccharides isolated from bronchial mucus glycoproteins of patients (blood group O) suffering from cystic fibrosis. (1987)
Breg J, Van Halbeek H, Vliegenthart J, Lamblin G, Houvenaghel M, Roussel P
Pubmed : 3665919  
Status : Reviewed

Structure determination of five sulfated oligosaccharides derived from tracheobronchial mucus glycoproteins. (1987)
Mawhinney TP, Adelstein E, Morris DA, Mawhinney AM, Barbero GJ
Pubmed : 3029097  
Status : Reviewed

Oligosaccharide structures of the low-molecular-weight salivary mucin from a normal individual and one with cystic fibrosis. (1985)
Reddy M, Levine M, Prakobphol A
Pubmed : 3855417   DOI : 10.1177/00220345850640010601
Status : Reviewed

Primary structure determination of five sialylated oliogsaccharides derived from bronchial mucus glycoproteins of patients suffering from cystic fibrosis. The occurrence of the NeuAc alpha(2---3)Gal beta(1---4)[Fuc alpha(1---3)] GlcNAc beta(1---.) structural element revealed by 500-MHz 1H NMR spectr (1984)
Lamblin G, Boersma A, Klein A, Roussel P, van Halbeek H, Vliegenthart J
Pubmed : 6746638  
Status : Reviewed

Further characterization, by a combined high-performance liquid chromatography/1H-NMR approach, of the heterogeneity displayed by the neutral carbohydrate chains of human bronchial mucins. (1984)
Lamblin G, Boersma A, Lhermitte M, Roussel P, Mutsaers J, van Halbeek H, Vliegenthart J
Pubmed : 6468389  
Status : Reviewed

Isolation and characterisation of neutral oligosaccharides from human bronchial glycoproteins. (1982)
Lamblin G, Lhermitte M, Boersma A, Roussel P, Van Halbeek H, Dorland L, Vliegenthart J
Pubmed : 7080930  
Status : Reviewed

Primary-structure determination of fourteen neutral oligosaccharides derived from bronchial-mucus glycoproteins of patients suffering from cystic fibrosis, employing 500-MHz 1H-NMR spectroscopy. (1982)
van Halbeek H, Dorland L, Vliegenthart J, Hull W, Lamblin G, Lhermitte M, Boersma A, Roussel P
Pubmed : 7140761  
Status : Reviewed